Malignant mixed ovarian germ cell tumour is a relatively rare tumour affecting young girl. It may be a threat to her future scope of fertility.
Case: A 13 years old girl reported with a large abdomino-pelvic mass along with enlarged para-aortic lymph nodes and raised beta-hCG, alfa-feto protein and lactate dehydrogenase levels. Fertility sparing surgery followed by four cycles of adjuvant chemotherapy was given to her. Her one year follow-up has been recurrence free.
Conclusion: Advanced malignant mixed ovarian germ cell tumour can be treated by fertility preserving cytoreductive surgery and adjuvant chemotherapy with good outcome.