Abstract: Introduction: The syndrome of obstructed hemi-vagina and ipsilateral renal anomaly (OHVIRA), also known as Herlyn-Werner-Wonderlich syndrome is a rare congenital anomaly of the Mullerian ducts (paramesonephric).
Presentation of case: In this report we present a rare case of HWWS diagnosed in a 16-year-old female presenting with cyclical abdominal pain and lump in lower after the onset of menarche, describe the various diagnostic modalities and treatment options available, along with a current review of the literature.
Discussion: Patients with HWWS usually present within 1 year after menarche with hematocolpos on the side of the obstructed hemi-vagina, producing abdominal pain, dysmenorrhea, and abdominal mass. An early and correct diagnosis is necessary to relieve the symptoms and prevent complications caused by retrograde menstruation which may lead to endometriosis and subsequently infertility
Conclusion: The purpose of this case report is to offer a better under-standing of the pathophysiology of HWWS so that when a young female presents with common, nonspecific symptoms, treating physicians may include HWWS on their list of differential diagnoses. Greater awareness of HWWS will lead to earlier detection and, consequently, reduced complications caused by delayed diagnosis
Indexed in Index Copernicus
